Focal fibrocartilaginous dysplasia of the femur: a case with spontaneous resolution
Abstract
Focal fibrocartilaginous dysplasia is a condition of unknown etiology associated with long bone deformities in children. Some authors recommend surgery as the initial treatment. The aim of this paper is to report a case of focal fibrocartilaginous dysplasia of the femur with spontaneous resolution and to review the literature. A case of a 2-month-old girl with varus deformity of the left femur and leg length discrepancy is reported. Radiographs showed a radiolucent area with marginal sclerosis and a varus deformity of 30º. Over a period of 22 months, complete spontaneous correction of the deformity was noticed. Twenty cases of femoral focal fibrocartilaginous dysplasia have been reported in the literature, 17 were treated surgically, three showed spontaneous correction. Patients should be monitored during a period longer than that recommended to avoid unnecessary invasive procedures.References
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