Analysis of dysplasia epiphysealis hemimelica (Trevor´s disease) of the ankle.

Keywords: Trevor’s disease, epiphyseal osteochondroma, ankle, endochondral ossification.

Abstract

Dysplasia epiphysealis hemimelica or Trevor’s disease is an osteocartilaginous deformity in the bone epiphyseal area. It is an uncommon condition prevailing in males. It develops in childhood, with growth plates still open, and it affects mainly patients’ ankles and knees. It is a condition of unknown origin. We present three cases with different degrees of severity, and also the therapeutic alternatives for each. There is only one case subject to surgical treatment due to irreducible equinus deformity. We provide details about surgical techniques, postoperative management and results in histologic analyses. We recommend operating on only those patients with some functional limitation or severe deformity due to the high recurrence rates they are associated with.

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Author Biographies

Matías Iglesias, Hospital de Trauma y Emergencias "Dr. Federico Abete", Buenos Aires
Servicio de Ortopedia y Traumatología, Hospital de Trauma y Emergencias  "Dr. Federico Abete", Buenos Aires
Martín Rofrano, Hospital de Trauma y Emergencias "Dr. Federico Abete", Buenos Aires
Servicio de Ortopedia y Traumatología, Hospital de Trauma y Emergencias  "Dr. Federico Abete", Buenos Aires
Enzo Sperone, Hospital de Trauma y Emergencias "Dr. Federico Abete", Buenos Aires
Servicio de Ortopedia y Traumatología, Hospital de Trauma y Emergencias  "Dr. Federico Abete", Buenos Aires
Alberto Macklin Vadell, Hospital de Trauma y Emergencias "Dr. Federico Abete", Buenos Aires
Servicio de Ortopedia y Traumatología, Hospital de Trauma y Emergencias  "Dr. Federico Abete", Buenos Aires
Alejandro Fazio, Hospital de Trauma y Emergencias "Dr. Federico Abete", Buenos Aires
Servicio de Ortopedia y Traumatología, Hospital de Trauma y Emergencias  "Dr. Federico Abete", Buenos Aires

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Published
2018-11-13
How to Cite
Iglesias, M., Rofrano, M., Sperone, E., Macklin Vadell, A., & Fazio, A. (2018). Analysis of dysplasia epiphysealis hemimelica (Trevor´s disease) of the ankle. Revista De La Asociación Argentina De Ortopedia Y Traumatología, 83(4), 291-297. https://doi.org/10.15417/issn.1852-7434.2018.83.4.794
Section
Case Presentations