Patient with Klippel-Trenaunay Syndrome. Case Report of an Intraoperatively Aborted Hip Joint Replacement

Keywords: Klippel-Trenaunay Syndrome, arteriovenous malformations, massive bleeding, hip

Abstract

Klippel-Trenaunay Syndrome is a rare congenital disorder. It usually affects one of the lower limbs. It is characterized by the presence of angiomas, venous malformations, hypertrophic varices with arteriovenous communications and hypertrophy of the affected limb, altering in some cases the bone structure. The aim of this presentation is to describe the case of a 54-year-old patient for whom a joint replacement of the left hip had been scheduled for one year and the surgery had to be aborted due to the risk of exsanguination of the patient, and to analyze the literature in this regard.

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Author Biographies

Fernando Adrián Lopreite, Orthopedics and Traumatology Service, Hospital Británico de Buenos Aires (Buenos Aires, Argentina)
Orthopedics and Traumatology Service, Hospital Británico de Buenos Aires (Buenos Aires, Argentina)
Joaquín Rodríguez, Orthopedics and Traumatology Service, Hospital Británico de Buenos Aires (Buenos Aires, Argentina)
Orthopedics and Traumatology Service, Hospital Británico de Buenos Aires (Buenos Aires, Argentina)
Fernando Tillet, Orthopedics and Traumatology Service, Hospital Británico de Buenos Aires (Buenos Aires, Argentina)
Orthopedics and Traumatology Service, Hospital Británico de Buenos Aires (Buenos Aires, Argentina)
Stefano Gaggiotti, Orthopedics and Traumatology Service, Hospital Británico de Buenos Aires (Buenos Aires, Argentina)
Orthopedics and Traumatology Service, Hospital Británico de Buenos Aires (Buenos Aires, Argentina)
Leonardo Matías Cullari, Orthopedics and Traumatology Service, Hospital Británico de Buenos Aires (Buenos Aires, Argentina)
Orthopedics and Traumatology Service, Hospital Británico de Buenos Aires (Buenos Aires, Argentina)
Hernán del Sel, Orthopedics and Traumatology Service, Hospital Británico de Buenos Aires (Buenos Aires, Argentina)
Orthopedics and Traumatology Service, Hospital Británico de Buenos Aires (Buenos Aires, Argentina)

References

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https://doi.org/10.1016/s0741-5214(95)70199-0

Published
2021-04-14
How to Cite
Lopreite, F. A., Rodríguez, J., Tillet, F., Gaggiotti, S., Cullari, L. M., & del Sel, H. (2021). Patient with Klippel-Trenaunay Syndrome. Case Report of an Intraoperatively Aborted Hip Joint Replacement. Revista De La Asociación Argentina De Ortopedia Y Traumatología, 86(2), 240-245. https://doi.org/10.15417/issn.1852-7434.2021.86.2.1108
Section
Case Presentations

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