Non-surgical management of osteopetrosis: two case reports an review of the literature

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Published: Nov 12, 2019
DOI: https://doi.org/10.15417/issn.1852-7434.2019.84.4.869
Keywords:
Osteoclasts, humerus fracture, osteopetrosis.

Main Article Content

Juan Carlos Caruso
Hospital Militar Central "Cirujano Mayor Doctor Cosme Argerich"–Hospital General 601, CABA, Argentina
http://orcid.org/0000-0001-6729-2771
Juan Martín Patiño
Hospital Militar Central "Cirujano Mayor Doctor Cosme Argerich" Hospital General 601, CABA, Argentina
http://orcid.org/0000-0002-9036-0442

Abstract

Osteopetrosis (also known as Albers-Schönberg disease) is a syndrome that includes four classic types and is characterized by bone dysplasia and lack of bone resorption due to abnormal osteoclastic activity and consequent development of brittle and hard bone that is prone to fractures that are difficult to treat surgically. Herein we present two cases of osteopetrosis with diaphyseal fractures of the humerus, both managed with non-surgical treatment. The objectives of our manuscript are to document our experience in the management of these cases and review the literature. The non-invasive treatment provides the best outcome for dyaphyseal fractures on the humerus in patients with osteopetrosis, given that the quality of the bone in these patients impairs the implementation of osteosynthesis. In addition, the placement of implants can lead to complications such as infections, delayed consolidation and pseudoarthrosis, among others. Surgical treatment should reserved for certain patients such as those with delayed consolidation, pseudoarthrosis, a history of repeated fractures, pre-existing deformity and those who are at risk for the development of disabling deformities or do not respond to non-surgical treatment

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How to Cite
Caruso, J. C., & Patiño, J. M. (2019). Non-surgical management of osteopetrosis: two case reports an review of the literature. Revista De La Asociación Argentina De Ortopedia Y Traumatología, 84(4), 386-392. https://doi.org/10.15417/issn.1852-7434.2019.84.4.869
Issue
Vol 84 No 4 (2019)
Section
Case Presentations
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Author Biographies

Juan Carlos Caruso, Hospital Militar Central "Cirujano Mayor Doctor Cosme Argerich"–Hospital General 601, CABA, Argentina

Especialista en Cirugia de la mano.Miembro Titular de la AAOT.Miembro Titular de la AACM.Miembro Titular de la AATO.

Juan Martín Patiño, Hospital Militar Central "Cirujano Mayor Doctor Cosme Argerich" Hospital General 601, CABA, Argentina

Jefe del servicio de cirugia de la mano Hospital Militar Central Dr. Cosme Argerich, CABA, Argentina Miembro Titular de la AAOT. Miembro Titular de la AACM.

References

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